Search on: PORPHOBILINOGEN SYNTHASE 
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Descriptor English:   Porphobilinogen Synthase 
Descriptor Spanish:   Porfobilinógeno Sintasa 
Descriptor Portuguese:   Sintase do Porfobilinogênio 
Synonyms English:   Aminolevulinate Hydro-Lyase
Aminolevulinic Acid Dehydratase  
Tree Number:   D08.811.520.241.300.550
Definition English:   An enzyme that catalyzes the formation of porphobilinogen from two molecules of 5-aminolevulinic acid. EC 4.2.1.24. 
Indexing Annotation English:   DF: ALA DEHYDRASE
History Note English:   98(73) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   633 
Unique Identifier:   D000623 

Occurrence in VHL:
 

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